Cardiomyopathy mimicking left ventricular noncompaction in a patient with lupus nephritis

dc.authorid0000-0001-9905-4305
dc.authorid0000-0001-5943-0302
dc.contributor.authorÖzkök, Abdullah
dc.contributor.authorAcar, Goksel
dc.contributor.authorElçioğlu, Ömer Celal
dc.contributor.authorBakan, Ali
dc.contributor.authorAtilgan, Kadir Gokhan
dc.contributor.authorSasak, Gulsah
dc.contributor.authorAlisir, Sabahat
dc.date.accessioned2025-05-10T19:48:09Z
dc.date.issued2012
dc.departmentİstanbul Medeniyet Üniversitesi
dc.description.abstractA 37-year-old female patient was admitted with exertional dyspnea. Her serum creatinine was 2.4 mg/dL and anti-nuclear antibody was positive in a titer of 1/320. Renal biopsy revealed diffuse proliferative lupus nephritis. Echocardiography and cardiac magnetic resonance (MR) imaging showed increased apical trabeculations compatible with left ventricular noncompaction (LVNC), which is a rare genetic cardiomyopathy. The patient expressed a marked improvement in exertional dyspnea after the immune-suppressive treatment for systemic lupus erythematosus (SLE). Control echocardiography revealed a significant increase of ejection fraction. SLE may cause a kind of cardiomyopathy with high resemblance to LVNC. Discrimination of these two similar clinical entities is important because SLE-induced cardiomyopathy is potentially reversible after the immune-suppressive treatment for SLE.
dc.identifier.doi10.1007/s13730-012-0015-4
dc.identifier.endpage72
dc.identifier.issn2192-4449
dc.identifier.issue2
dc.identifier.pmid28509061
dc.identifier.scopusqualityQ3
dc.identifier.startpage69
dc.identifier.urihttps://doi.org/10.1007/s13730-012-0015-4
dc.identifier.urihttps://hdl.handle.net/20.500.14730/11606
dc.identifier.volume1
dc.identifier.wosWOS:000218804500002
dc.identifier.wosqualityN/A
dc.indekslendigikaynakWeb of Science
dc.indekslendigikaynakPubMed
dc.language.isoen
dc.publisherSpringer Japan Kk
dc.relation.ispartofCen Case Reports
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanı
dc.rightsinfo:eu-repo/semantics/openAccess
dc.snmzKA_WOS_20250302
dc.subjectLeft ventricular noncompaction
dc.subjectSystemic lupus erythematosus
dc.subjectCardiomyopathy
dc.subjectLupus nephritis
dc.titleCardiomyopathy mimicking left ventricular noncompaction in a patient with lupus nephritis
dc.typeArticle

Dosyalar

Orijinal paket

Listeleniyor 1 - 1 / 1
Yükleniyor...
Küçük Resim
İsim:
11606.pdf
Boyut:
251.89 KB
Biçim:
Adobe Portable Document Format